試題詳解

【已刪除】77. A deficiency of branched chain α-keto acid dehydrogenease complex causes the defect in metabolism of amino acids. The accumulation of α-keto acid in urine leads to maple syrup urine disease. Which of the following amino acids are metabolized by α-keto acid dehydrogenease complex? ① Methionine ② Leucine ③ Isoleucine ④ Valine ⑤ Alanine
(A) ①②⑤
(B) ①③⑤
(C) ②③④
(D) ②④⑤
(E) ③④⑤