87. 一位七歲大男童患有遺傳性球型紅血球症(congenital sphero..-阿摩線上測驗
1F Yen-Ju Chu 小一下 (2016/06/13)
Children with HS are susceptible to aplastic crises, a result of parvovirus B19 infection and hypoplastic crises associated with various other infections. High RBC turnover + erythroid marrow failure => profound anemia (hematocrit <10%), high-output heart failure, cardiovascular collapse, and death. Rare complications associated with HS include splenic sequestration crisis, gout, cardiomyopathy, priapism, leg ulcers, and spinocerebellar degeneration. |