70.一名20歲女孩因美觀問題求診,她的前牙已嚴重磨耗,後牙的根尖片如圖。除了她之外,她的母親和妹妹 也都有類似情形。她們可能罹患下列何種疾病?
(A)amelogenesis imperfecta
(B)dentinogenesis imperfecta
(C)dentin dysplasia
(D)odontogenesis imperfecta
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統計: A(59), B(339), C(38), D(33), E(0) #1032405
統計: A(59), B(339), C(38), D(33), E(0) #1032405
詳解 (共 4 筆)
#2336820
B) Dentinogenesis Imperfecta
中胚層障礙,外胚層正常。萌發時外型正常,但牙釉質容易一片片剝落,且暴露牙本質快速attrition;pulp chamber & root canals obliteration(堵塞),bulbous crowns, cervical constriction, thin roots.
C) Dentinal Dysplasia
無根牙(rootless tooth), 牙釉質正常,牙本質不正常,堵塞齒髓。
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#6523724
如何鑑別DD type II與DI
相同處: crown with altered color and obliterated pulp chambers
相異處:
- DD type II較易有thistle tube-shaped canal
- DI通常是花苞狀牙冠、齒頸部收縮;DD type II牙冠通常是正常的
- periapical rarefying osteitis 較常見於DD
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