87. 一位七歲大男童患有遺傳性球型紅血球症(congenital spherocytosis)，最近三日來感覺精神不佳。理學檢查發現心跳每分鐘190下， 呼吸每分鐘50下，臉色十分蒼白。實驗室檢查顯示Hb: 3.2mg/dl, WBC: 5400/mm3，Platelets: 160,000/mm3, reticulocyte: 0.8%,以下何者為最可能的解釋？
(A)急性失血。
(B)Aplastic crisis。
(C)Hyperhemolytic crisis。
(D)Splenic sequestration crisis。
(E)Vaso-occlusive crisis。

答案：登入後查看
統計： A(2), B(18), C(7), D(9), E(2) #1125794

詳解 (共 1 筆)

#1380413
Children with HS are susceptible to aplastic crises, a result of parvovirus B19 infection and hypoplastic crises associated with various other infections. 
High RBC turnover + erythroid marrow failure
=> profound anemia (hematocrit <10%), high-output heart failure, cardiovascular collapse, and death. 
Rare complications associated with HS include splenic sequestration crisis, gout, cardiomyopathy, priapism, leg ulcers, and spinocerebellar degeneration.
4
0