46 一位 21 歲女性,因陰蒂肥大求診,被診斷為 congenital adrenal hyperplasia(CAH),其血中 17-hydroxyprogesterone(17-HP)為 600 ng/dL。下列關於 CAH 之病因及治療的敘述,何者最適當?
(A)最常見為 21-hydroxylase deficiency,治療最有效為 cortisone
(B)最常見為 11β-hydroxylase deficiency,治療最有效為 dexamethasone
(C)最常見為 21-hydroxylase deficiency,治療最有效為 dexamethasone
(D)最常見為 11β-hydroxylase deficiency,治療最有效為 cortisone

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統計: A(21), B(3), C(18), D(0), E(0) #1095655